juvenile granulosa cell tumor


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  • Clinical

    • testicular
      • 30% involves abdominal testis
      • perinatal presentation
      • genital abnormalities
  • Histology

    • cystic
    • lining: granulosa cells (inner), theca cells (outer)
    • occasional Call-Exner bodies
  • Stains

    • granulosa cells: vimentin, CK, S100, focal anti-mullerian hormone
    • theca cells: vimentin, SMA, focal desmin