low grade fibromyxoid sarcoma


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  • Clinical

    • site: trunk, proximal extremities

  • Histology

    • collagen, myxoid
    • bland spindle cells, whirling
    • curvilinear vessels
    • variants
      • Classical
      • Giant collagen rosettes
        • central hyalinized collagen
        • cuff of epithelioid fibroblasts
      • prognosis is the same

  • Stains

    • pos: EMA (80%, at least focal), MUC4
    • vimentin+
    • occasional focal actin+
    • negative: desmin, S100, CK, CD34
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