infantile fibrosarcoma
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Clinical- age: infants, young children
- site: extremities, trunk, head and neck. Rarely mesentery or retroperitoneal
- prognosis: rarely metastasize, better outcome than adult fibrosarcoma
Histology- poorly circumscribed, infiltrative
- herringbone fascicles, densely cellular
- ovoid and spindle cells
- necrosis, hemorrhage, calcifications
Stains- vimentin+
- variable for NSE, actin
- usually negative for desmin, S100, CD34
Molecular- ETV6/NTRK3 fusion, t(12;15)(p13;q26)
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