diffuse pulmonary lymphangiomatosis


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  • Clinical

    • young age
    • asthma

  • Histology

    • diffuse
    • anastamosing lymphovascular spaces
    • spindle cells

  • Stains

    • endothelial+
    • spindle cells
      • positive for vimentin, desmin, actin, PR
      • negative for ER, CK, HMB45

  • Ddx

    • lymphangiectasis
    • lymphangioleiomyomatosis
    • Kaposi sarcoma
    • diffuse pulmonary hemangiomatosis
      • spaces are blood filled
      • lacks spindle cells
    		•